-
A Case of Autoimmune Inner Ear Disease Mimicking Bilateral Ménièreʼs Disease
-
Hong-Ju Kim, Yoon-Gi Choi, HyunJi Kim, Kyu-Sung Kim
-
Received February 1, 2018 Accepted March 8, 2018 Published online March 8, 2018
-
[Accepted]
-
-
 Abstract
- Autoimmune inner ear disease(AIED) is a rare disease, accounting for <1% of all case of hearing impairment or dizziness. It is characterized by sensorineural hearing loss(SNHL) or vestibular dysfunction that result from an immune-mediated process. Clinical feature of AIED is SNHL that progresses over weeks to months and fluctuating hearing symptoms. Because there’s no diagnostic laboratory test, clinical features and re-sponse to immunosuppressive therapy were important for diagnosis of AIED. Many disease such as sudden sensorineural hearing loss and Meniere's disease may also mimic AIED, a broad differential must be maintained in patients suspected of having AIED. We report a case of a 46-year-old female who presented with sudden hearing loss and vertigo. We could diagnose her as AIED with systemic lupus erythematous(SLE). The symptoms were improved treated with steroids.
|
KBS
